phytanoyl-CoA 2-hydroxylase, ELISA Kit

Rat Phytanoyl-CoA dioxygenase; peroxisomal (PHYH) ELISA kit; RP11-24J20.1; LN1; LNAP1; PAHX; PHYH1; RD; phytanic acid oxidase; phytanoil-CoA alpha hydroxylase; phytanoyl-CoA 2 oxoglutarate dioxygenase; phytanoyl-CoA alpha-hydroxylase; phytanoyl-CoA dioxygenase; p; phytanoyl-CoA 2-hydroxylase

For Research Use Only. Not for use in diagnostic procedures.

Store all reagents at 2-8 degree C

Select online data sheet information is drawn from bioinformatics databases, occasionally resulting in ambiguous or non-relevant product information. It is the responsibility of the customer to review, verify, and evaluate the information to make sure it matches their requirements before purchasing the kit. Our ELISA Kit assays are dynamic research tools and sometimes they may be updated and improved. If the format of this assay is important to you then please request the current manual or contact our technical support team with a presales inquiry before placing an order. We will confirm the current details of the assay. We cannot guarantee the sample manual posted online is the most current manual.

Small volumes of PHYH elisa kit vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.

MBS9333846 is a ready-to-use microwell, strip plate ELISA (enzyme-linked immunosorbent assay) Kit for analyzing the presence of the phytanoyl-CoA 2-hydroxylase (PHYH) ELISA Kit target analytes in biological samples. The concentration gradients of the kit standards or positive controls render a theoretical kit detection range in biological research samples containing PHYH. The ELISA analytical biochemical technique of the MBS9333846 kit is based on PHYH antibody-PHYH antigen interactions (immunosorbency) and an HRP colorimetric detection system to detect PHYH antigen targets in samples. The ELISA Kit is designed to detect native, not recombinant, PHYH. Appropriate sample types may include undiluted body fluids and/or tissue homogenates, secretions. Quality control assays assessing reproducibility identified the intra-assay CV (%) and inter-assay CV(%).

38,588 Da

phytanoyl-CoA 2-hydroxylase

phytanoyl-CoA dioxygenase, peroxisomal; phytanic acid oxidase; phytanoyl-CoA alpha-hydroxylase; phytanoyl-CoA hydroxylase (Refsum disease)

Phytanoyl-CoA dioxygenase, peroxisomal

PhyH  [Similar Products]

PAHX_RAT

catalyzes the conversion of phytanoyl-CoA to 2-hydroxyphytanoyl-CoA; plays a role in phytanic acid alpha-oxidation [RGD, Feb 2006]

PHYH: Converts phytanoyl-CoA to 2-hydroxyphytanoyl-CoA. Defects in PHYH are a cause of Refsum disease (RD). RD is an autosomal recessive disorder characterized clinically by a tetrad of abnormalities: retinitis pigmentosa, peripheral neuropathy, cerebellar ataxia, and elevated protein levels in the cerebrospinal fluid (CSF). Patients exhibit accumulation of the branched-chain fatty acid, phytanic acid, in blood and tissues. Less constant features are nerve deafness, anosmia, skeletal abnormalities, ichthyosis, cataracts and cardiac impairment. Manifestations of the disease appear in the second or third decade of life. Belongs to the PhyH family.

Protein type: Oxidoreductase; EC 1.14.11.18

Cellular Component: mitochondrion; peroxisome

Molecular Function: L-ascorbic acid binding; metal ion binding; cofactor binding; catalytic activity; phytanoyl-CoA dioxygenase activity

Biological Process: isoprenoid metabolic process; fatty acid alpha-oxidation

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