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1,4-Alpha-Glucan-Branching Enzyme (GBE1) Antibody

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产品名称: 1,4-Alpha-Glucan-Branching Enzyme (GBE1) Antibody
产品型号: abx002344
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简单介绍

1,4-Alpha-Glucan-Branching Enzyme (GBE1) Antibody


1,4-Alpha-Glucan-Branching Enzyme (GBE1) Antibody  的详细介绍
GBE1 Antibody is a Rabbit Polyclonal antibody against GBE1. The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease).

Target GBE1
Reactivity Human, Mouse
Host Rabbit
Clonality Polyclonal
Tested Applications WB, IF/ICC
Recommended dilutions WB: 1/1000 - 1/2000, IF/ICC: 1/20 - 1/50. Optimal dilutions/concentrations should be determined by the end user.
Immunogen Recombinant protein of human GBE1.
Purification Affinity purified.
Form Liquid
Isotype IgG
Conjugation Unconjugated
Storage Store at 4 °C.
Molecular Weight Calculated MW: 80 kDa
Observed MW: 80 kDa
Swiss Prot Q04446
GeneID 2632
Gene Symbol GBE1
Concentration > 1 mg/ml
Buffer PBS, pH 7.3, 0.02% sodium azide.
UNSPSC Code 12352203
Availability Shipped within 5-10 working days.
Note This product is for research use only.
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